ICD-11 code 2F32.2 refers to Meigs’ syndrome, a rare condition characterized by a triad of symptoms including a benign ovarian tumor, ascites (fluid buildup in the abdomen), and pleural effusion (fluid buildup around the lungs). Meigs’ syndrome is considered a diagnosis of exclusion, meaning other potential causes of the symptoms must be ruled out before it can be confirmed.
The exact cause of Meigs’ syndrome is unknown, but it is thought to be related to the release of fluid from the ovarian tumor into the abdominal and pleural cavities. The condition typically presents with symptoms such as abdominal bloating, discomfort, and difficulty breathing due to the fluid accumulation. Meigs’ syndrome can be difficult to diagnose, as it closely mimics other medical conditions such as ovarian cancer.
Treatment for Meigs’ syndrome typically involves surgical removal of the ovarian tumor, which often leads to resolution of the symptoms. In some cases, a hysterectomy may also be performed to prevent recurrence of the syndrome. The prognosis for patients with Meigs’ syndrome is generally favorable, with most individuals experiencing full recovery following appropriate treatment.
Table of Contents:
- #️⃣ Coding Considerations
- 🔎 Symptoms
- 🩺 Diagnosis
- 💊 Treatment & Recovery
- 🌎 Prevalence & Risk
- 😷 Prevention
- 🦠 Similar Diseases
#️⃣ Coding Considerations
The SNOMED CT code equivalent to the ICD-11 code 2F32.2, which represents Meigs’ syndrome, is 204598001. Meigs’ syndrome is a rare condition characterized by the presence of a triad of ascites, pleural effusion, and a benign ovarian tumor known as a fibroma. This syndrome was first described by the American gynecologist Joe Vincent Meigs in 1937. Despite being a benign condition, Meigs’ syndrome can present with symptoms such as abdominal distension, dyspnea, and pelvic pain due to the buildup of fluid in the abdomen and chest cavities. The diagnosis of Meigs’ syndrome is typically made based on clinical symptoms, imaging studies, and laboratory tests. Treatment usually involves surgical removal of the ovarian tumor, which results in resolution of the ascites and pleural effusion.
In the United States, ICD-11 is not yet in use. The U.S. is currently using ICD-10-CM (Clinical Modification), which has been adapted from the WHO’s ICD-10 to better suit the American healthcare system’s requirements for billing and clinical purposes. The Centers for Medicare and Medicaid Services (CMS) have not yet set a specific date for the transition to ICD-11.
The situation in Europe varies by country. Some European nations are considering the adoption of ICD-11 or are in various stages of planning and pilot studies. However, as with the U.S., full implementation may take several years due to similar requirements for system updates and training.
🔎 Symptoms
Meigs’ syndrome, classified as ICD-10 code 2F32.2, is a rare medical condition characterized by the triad of benign ovarian tumor, ascites, and pleural effusion. The presence of these three components distinguish Meigs’ syndrome from other differential diagnoses, such as malignant ovarian tumors or cirrhosis-related fluid accumulation.
One of the hallmark symptoms of Meigs’ syndrome is the development of an ovarian fibroma, which is typically a benign tumor that arises from the connective tissue of the ovary. These tumors may grow to a considerable size and cause symptoms such as pelvic pain, pressure, or discomfort. In some cases, the tumor may compress nearby structures, leading to urinary symptoms or constipation.
Another key feature of Meigs’ syndrome is the accumulation of fluid in the peritoneal cavity, known as ascites. Ascites is a common complication of various medical conditions, including liver cirrhosis, heart failure, and certain cancers. In the context of Meigs’ syndrome, ascites develops due to peritoneal irritation caused by the ovarian tumor, leading to an increase in fluid production within the abdominal cavity. The presence of ascites contributes to abdominal distension, discomfort, and difficulty breathing.
Pleural effusion, which is the accumulation of fluid in the pleural cavity surrounding the lungs, is the third component of Meigs’ syndrome. The fluid buildup in the pleural space can cause symptoms like shortness of breath, coughing, chest pain, and reduced lung function. Pleural effusion in Meigs’ syndrome is believed to result from the spread of fluid from the peritoneal cavity through diaphragmatic defects or lymphatic channels, leading to respiratory complications in affected individuals.
🩺 Diagnosis
Diagnosis of Meigs’ syndrome, classified under 2F32.2 in the ICD-10 coding system, typically involves a thorough medical history review and physical examination by a healthcare provider. Patients may present with symptoms such as abdominal distension, pleural effusion, and ascites, which are indicative of this rare syndrome. Laboratory tests such as complete blood count, serum chemistry panel, and tumor markers may be ordered to assess for underlying causes such as ovarian fibroma or thecomas.
Imaging studies such as ultrasound, MRI, or CT scans play a crucial role in the diagnosis of Meigs’ syndrome. These tests help visualize the presence of ovarian tumors, ascites, and pleural effusion, which are characteristic findings of the syndrome. The imaging findings can aid in distinguishing Meigs’ syndrome from other conditions that present with similar symptoms, such as ovarian cancer or heart failure.
In some cases, a diagnostic thoracentesis and/or paracentesis may be performed to analyze the pleural fluid and peritoneal fluid, respectively. Analyzing the fluid for cell count, protein levels, and cytology can help confirm the presence of Meigs’ syndrome. Additionally, a tissue biopsy may be recommended if there is suspicion of an underlying malignant or benign tumor. The combination of these diagnostic methods helps healthcare providers accurately diagnose Meigs’ syndrome and develop an appropriate treatment plan for affected individuals.
💊 Treatment & Recovery
Treatment for Meigs’ syndrome, also known as 2F32.2, typically involves surgery to remove the tumor causing the symptoms. The primary goal of surgery is to resect the tumor, typically an ovarian fibroma, while preserving the normal ovary and uterus if possible. In cases where the tumor is benign and confined to one ovary, a unilateral salpingo-oophorectomy may be performed to remove the affected ovary and fallopian tube.
For patients with Meigs’ syndrome who are not candidates for surgery or who have advanced disease, chemotherapy may be recommended as an alternative treatment option. Chemotherapy can help shrink the tumor and improve symptoms, particularly in cases where the tumor is malignant. Additionally, if the tumor is found to be cancerous, adjuvant therapy such as radiation therapy may also be considered to target any remaining cancer cells after surgery.
Recovery from surgery for Meigs’ syndrome can vary depending on the extent of the surgery and the overall health of the patient. Patients may experience post-operative pain, fatigue, and temporary limitations on physical activities. Additionally, close follow-up with healthcare providers is essential to monitor for any signs of recurrence or complications. With proper management and adherence to treatment recommendations, many patients are able to recover fully and resume their normal activities following treatment for Meigs’ syndrome.
🌎 Prevalence & Risk
In the United States, Meigs’ syndrome is considered to be a rare condition, with an estimated prevalence of less than 1 in 100,000 individuals. This means that only a small number of cases are reported each year in the country. The rarity of the syndrome can make it difficult to diagnose, as healthcare providers may not encounter it frequently.
In Europe, the prevalence of Meigs’ syndrome is also thought to be low, with similar estimates to those in the United States. Due to the rarity of the condition, there may be regional variations in the number of cases reported. In some parts of Europe, healthcare providers may be more familiar with Meigs’ syndrome and its symptoms, leading to more accurate diagnoses.
In Asia, Meigs’ syndrome is believed to be even less common compared to the United States and Europe. The prevalence of the syndrome in Asian countries may be slightly lower than in other regions. Limited data is available on the exact number of cases of Meigs’ syndrome in Asia, but it is generally considered to be a rare condition throughout the continent.
In Africa, Meigs’ syndrome is also rare, with prevalence rates similar to those in the United States, Europe, and Asia. The lack of awareness about the syndrome among healthcare providers in some African countries may lead to underdiagnosis or misdiagnosis of cases. Further research is needed to better understand the prevalence of Meigs’ syndrome in Africa and other regions of the world.
😷 Prevention
Meigs’ syndrome is a rare condition characterized by the triad of ascites, pleural effusion, and benign ovarian tumor. The most effective way to prevent Meigs’ syndrome is to promptly diagnose and surgically remove any ovarian tumors that may be present. Regular gynecological exams and ultrasounds can help detect ovarian tumors early on, increasing the likelihood of successful treatment and preventing the development of Meigs’ syndrome.
In addition to ovarian tumors, other conditions such as fibroids and endometriosis can also contribute to the development of ascites and pleural effusion. To prevent these conditions from progressing to Meigs’ syndrome, it is essential for women to maintain regular visits with their gynecologist and address any concerning symptoms promptly. Early intervention and treatment can help reduce the risk of complications associated with these conditions and help prevent the development of Meigs’ syndrome.
Overall, the key to preventing Meigs’ syndrome lies in early detection and timely treatment of underlying conditions such as ovarian tumors, fibroids, and endometriosis. By staying vigilant about their gynecological health and seeking medical attention for any concerning symptoms, women can reduce their risk of developing Meigs’ syndrome and its associated complications. Regular screenings and consultations with healthcare providers are crucial in maintaining optimal reproductive health and preventing the onset of Meigs’ syndrome.
🦠 Similar Diseases
Meigs’ syndrome, identified by the ICD-10 code 2F32.2, is a rare condition characterized by a triad of benign ovarian tumor, ascites, and pleural effusion. Although other diseases may present with similar symptoms, each condition has its unique characteristics that differentiate it from Meigs’ syndrome. One comparable disease is pseudomyxoma peritonei, categorized as C78.6 in the ICD-10, characterized by mucinous ascites and implants on peritoneal surfaces.
Another disease similar to Meigs’ syndrome is ovarian cancer, specifically ovarian malignant neoplasm, classified as C56 in the ICD-10. Ovarian cancer can also present with ascites and pleural effusion, but unlike Meigs’ syndrome, it involves malignant growth of ovarian tissue. Additionally, ovarian cancer typically causes symptoms such as abdominal bloating, pelvic pain, and urinary urgency, which are not commonly seen in Meigs’ syndrome.